诊断
需根据反复感染的病史和体格检查进行诊断。血液检查和基因检测或可确认诊断结果。
治疗
XLA 尚无治愈方法。治疗的目标是增强免疫系统以预防感染。在发生感染时,也可针对感染进行快速治疗。
药物
治疗 XLA 的药物包括:
医疗护理专业人员可能会建议您每 6 到 12 个月复诊一次,以筛查 XLA 的并发症。还可能建议您不要接种活疫苗,例如脊髓灰质炎、麻疹-流行性腮腺炎-风疹或水痘活疫苗。
临床试验
探索 Mayo Clinic 的研究 测试新的治疗、干预与检查方法,旨在预防、检测、治疗或控制这种疾病。
April 17, 2024
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